Preparation for cardiac catheterisation, Wolfram Scheible für Nationales Register © Wolfram Scheible für Nationales Register

Media

Congenital Heart Defects

Clinical relevance, survival and incidence

Congenital heart defects are the most common congenital malformation. In Germany, around 7,000 children are born with such defects every year. More than 90 percent of patients reach adulthood. More than 500,000 children, adolescents and adults in Germany are living with the underlying disease.

  • Extrapolated

    Development of clinical relevance

    Projections show that the clinical relevance of congenital heart disease will continue to increase in the coming years.

    Estimated clinical relevance of CHD in the next years



    • Live births with CHD 0.8% of all live births
    • Children with CHD 90% of live births with CHD
    • 18-year-old with CHD 80% of children with CHD
    • Adults with CHD

    Source: Competence Network for Congenital Heart Defects. Estimated values from 2000

    collapse

  • Good to know

    Survival rate development

    In Germany, around 7,000 children are born with a heart defect every year. Congenital malformations of the heart or large vessels are very diverse. They range from simple defects that have little effect on the cardiovascular system to very serious heart diseases that can lead to death if left untreated. Thanks to advances in paediatric cardiology, heart surgery and anaesthesia, more than 90 percent of patients now reach adulthood. In most cases, however, patients are chronically ill for life. Surgery is often followed by complications that can reduce quality of life, limit performance and work capacity, and even be life-threatening. The number of children, adolescents and adults affected - currently more than 500,000 in Germany - is constantly on the increase, because there is no cure in the true sense of the word.

    Überlebensrate der Kinder mit angeborenen Herzfehlern



    Source: Competence Network for Congenital Heart Defects.

    collapse

  • Übersicht

    Häufigkeit einzelner angeborener Herzfehler

    The frequency with which different heart defects occur varies greatly. There are simple heart defects and severe heart defects, which occur more frequently, but also moderate and severe heart defects, which occur very rarely. The following table gives an overview of the proportion of each diagnosis in the total number of congenital heart defects.

    VSD Ventricular septal defect (interventricular septal defect) 31 %
    ASD Atrial septal defect 7 %
    PDA Persistent ductus arteriosus 7 %
    PaV Pulmonary valve stenosis 7 %
    ISTA Coarctation of the aorta 5 - 8 %
    AoV Aortic valve stenosis 3 - 6 %
    TOF Tetralogy of Fallot 5,5 %
    AVSD Atrioventricular septal defect 4,8 %
    TGA Transposition of the great arteries 4,5 %
    HLHS Hypoplastic left heart syndrome 3,8 %
    PA+VSD Pulmonary atresia with ventricular septal defect 2,5 - 3,4 %
    PA Pulmonary atresia without ventricular septal defect 2,4 %
    TrA Tricuspid atresia 1 - 2 %
    DIV Double inlet ventricle (single ventricle) 1,5 %
    DORV Double outlet right ventricle 1,2 %
    ccTGA Congenitally corrected transposition of the great arteries 1 %
    TAC Truncus arteriosus communis 0,5 - 1 %
    HOCM hypertrophic obstructive cardiomyopathy 0,4 %
    Suprav. AS Supravalvular aortic stenosis (Williams-Beuren syndrome) 0,4 %
    collapse

Share this page via ...